McCune-Albright Syndrome revealed by maxillary pain in adulthood: a review and case report

Document Type : Case Report

Authors

Oral and maxillofacial surgery department, Hassan II University Hospital, Sidi Mohamed Ben Abdellah University, Faculty of Medicine and Pharmacy, Fes, Morocco

Abstract

McCune - Albright syndrome is a rare sporadic disease defined by the triad: café-au-lait spots, fibrous bone dysplasia and endocrinopathy We report the case of a McCune - Albright syndrome of fortuitous discovery in a 70-year-old patient referred to the OMFS department for the management of chronic right maxillary pain, associated with headache, homolateral lacrimation and nasal obstruction. The examination of our patient reveals a facial asymmetry due to a maxillary tumefaction, a median mass mobile on swallowing, and cafe-au-lait spots of right scapular and abdominal regions. Facial CT scan shows an osteolytic and osteocondensing process of the right maxilla with extension to the nasal cavity and the hard palate. Cervical ultrasound found a multinodular goiter, with subclinical hyperthyroidism on thyroid checkup. The association of FD, hyperthyroidism, and cafe-au-lait spots classified the patient as a carrier of McCune-Albright syndrome. We opted for maxillary shaping surgery to meet the aesthetic demand and to improve the respiratory function of our patient. Histological examination confirmed the diagnosis of fibrous dysplasia. Follow-up of the patient after 2 years showed a disappearance of the maxillary pain and nasal obstruction with restoration of facial symmetry.

Keywords

Egyptian Journal of Oral and Maxillofacial Surgery
Volume 16, Issue 4
October 2025
Pages 218-221

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History

  • Receive Date: 08 March 2025
  • Accept Date: 08 May 2025

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